Popliteal Pterygium Syndrome at the Mother and Child University Hospital Lagune of Cotonou: Epidemiological, Clinical and Therapeutic Aspects
Gbenou AS, Koco H*, Padonou B, Assan BR, Assouto CBU, Fiogbé MA and Uroz Tristan J
Introduction: Congenital webbing knee or popliteal pterygium is the tissue filling the posterior aspect of the joint limiting extension. It can be part of several syndromes including the popliteal pterygium syndrome (SPP).
Purpose: To present the cases of patients suffering from
Patient and Method: This is a description of epidemiologica, clinical and therapeuticaspects of clinical cases of webbing admitted to our unit over 10 years.
Result: There were four girls and two boys. The average age was 8±3, 93 years with extremes of 3 and 15 years. Ten knees were involved. The webbing was knee-ankle- leg (7 cases) and hamstring leg (3 cases). The march was limping (2 cases) or lap (4 cases). Associated malformations were identified, sacral agenesis of vertebrae (3 cases), hypoplasia of the labia majora (2 cases) and incontinence of urine (1 case), bilateral cryptorchidism (3 cases), orofacial anomalies (3) and clubfoot (5). Surgery which was followed by equipment, were musculo -cutaneous plasty in the popliteal fossa (3 cases) or a leg amputation (4 cases).
Conclusion: The popliteal syndrome is the most important malformation of SPP, purveyor of disability, requiring screening and early orthopedic support that would limit the indication for amputation.